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| LETTER TO THE EDITOR |
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| Year : 2022 | Volume
: 2
| Issue : 2 | Page : 641 |
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Response to comment on: Management of microspherophakia and angle-closure glaucoma in Goldenhar syndrome
Vijayalakshmi A Senthilkumar1, Chinmayee Pradhan1, Sharmila Rajendrababu1, Chitaranjan Mishra2, Naresh B Kannan2
1 Department of Glaucoma, Aravind Eye Hospital and Postgraduate Institute of Ophthalmology, Madurai, Tamil Nadu, India
2 Department of Retina and Vitreoretinal Surgery, Aravind Eye Hospital and Postgraduate Institute of Ophthalmology, Madurai, Tamil Nadu, India
| Date of Web Publication | 13-Apr-2022 |
Correspondence Address:
Sharmila Rajendrababu
Glaucoma Consultant, Department of Glaucoma, Aravind Eye Hospital and Postgraduate Institute of Ophthalmology, Tamil Nadu
India
 Source of Support: None, Conflict of Interest: None
DOI: 10.4103/ijo.IJO_526_22
How to cite this article:
Senthilkumar VA, Pradhan C, Rajendrababu S, Mishra C, Kannan NB. Response to comment on: Management of microspherophakia and angle-closure glaucoma in Goldenhar syndrome. Indian J Ophthalmol Case Rep 2022;2:641 |
How to cite this URL:
Senthilkumar VA, Pradhan C, Rajendrababu S, Mishra C, Kannan NB. Response to comment on: Management of microspherophakia and angle-closure glaucoma in Goldenhar syndrome. Indian J Ophthalmol Case Rep [serial online] 2022 [cited 2022 May 27];2:641. Available from: https://www.ijoreports.in/text.asp?2022/2/2/641/342998 |
Dear Editor,
We thank the authors for their valuable inputs and providing us an opportunity for clarifying our case report further.[1] We do agree with the authors that typical presentation of Goldenhar syndrome includes epibulbar dermoids, microtia, mandibular hypoplasis, and vertebral anomalies.[1],[2] Published literature search has shown few case reports describing preauricular tags and epibulbar or limbal dermoid without any hemifacial microsomia or vertebral malformation as the clinical features of Goldenhar syndrome.[3] In a case report by Juneja et al.,[3] the authors have mentioned that patients with Goldenhar syndrome may present with auricular and ocular features alone, though hemifacial microsomia and vertebral malformations are frequent associations. The patient in our published report had preauricular tags and limbal dermoid, similar to the report by Juneja et al.[3]
The purpose of publishing this case report was to emphasize the rare ocular association of limbal dermoids with microspherophakia and advanced glaucomatous disk damage in a young patient.[4] Further, our main concern was to preserve the vision-threatening bilateral glaucomatous disease in a young patient by early surgical intervention. Presence of limbal dermoids can be technically challenging to the operating vitreoretinal and glaucoma surgeons if pars plana lensectomy with scleral fixated intraocular lens with aqueous drainage implant is planned.
Acknowledgement
Mr. Rajkumar, photographer, Aravind eye hospital, Madurai, India is acknowledged.
Financial support and sponsorship
Nil.
Conflicts of interest
There are no conflicts of interest.
| References | |  |
| 1. | Chauhan A, Sharma DK. Comment on: Management of microspherophakia and angle-closure glaucoma in Goldenhar syndrome. Indian J Ophthalmol Case Rep 2022;2:640.  [Full text] |
| 2. | Gathwala G, Tiwari AD, Singh I, Yadav SP. Goldenhar's syndrome. Indian J Pediatr 1992;59:770-2. |
| 3. | Juneja A, Puthalath AS, Gupta N, Verma PK. Isolated bilateral limbal dermoid, preauricular skin tags and ametropic amblyopia. BMJ Case Rep 2021;14:e245078. |
| 4. | Senthilkumar VA, Pradhan C, Rajendrababu S, Mishra C, Kannan NB. Management of microspherophakia and angle-closure glaucoma in Goldenhar syndrome. Indian J Ophthalmol Case Rep 2022;2:98-100. [Full text] |
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