|Year : 2021 | Volume
| Issue : 4 | Page : 872
A rare case report of isolated bilateral congenital ectropion uveae without secondary glaucoma
Shruthy Vaishali Ramesh1, Prasanna Venkatesh Ramesh2, Ramesh Rajasekaran3, Meena Kumari Ramesh4
1 Medical Officer, Department of Cataract and Refractive Surgery, Mahathma Eye Hospital Private Limited, Trichy, Tamil Nadu, India
2 Medical Officer, Department of Glaucoma and Research, Mahathma Eye Hospital Private Limited, Trichy, Tamil Nadu, India
3 Chief Medical Officer, Mahathma Eye Hospital Private Limited, Trichy, Tamil Nadu, India
4 Head of the Department of Cataract and Refractive Surgery, Mahathma Eye Hospital Private Limited, Trichy, Tamil Nadu, India
|Date of Web Publication||09-Oct-2021|
Dr, Prasanna Venkatesh Ramesh
Mahathma Eye Hospital Private Limited, No 6, Tennur, Seshapuram, Trichy - 620 017, Tamil Nadu
Source of Support: None, Conflict of Interest: None
|How to cite this article:|
Ramesh SV, Ramesh PV, Rajasekaran R, Ramesh MK. A rare case report of isolated bilateral congenital ectropion uveae without secondary glaucoma. Indian J Ophthalmol Case Rep 2021;1:872
|How to cite this URL:|
Ramesh SV, Ramesh PV, Rajasekaran R, Ramesh MK. A rare case report of isolated bilateral congenital ectropion uveae without secondary glaucoma. Indian J Ophthalmol Case Rep [serial online] 2021 [cited 2021 Oct 21];1:872. Available from: https://www.ijoreports.in/text.asp?2021/1/4/872/327647
An 18-year-old male with best-corrected visual acuity of 20/20 oculus uterque (OU) and intraocular pressure in the low-teens OU, presented with anterior segment findings of bilateral ectropion uveae [Figure 1] and normal angles on gonioscopy with few iris processes [Figure 2]; with no evidence of anterior synechiae, abnormal iris insertion or dysgenesis, or neovascularization [Figure 2]. The patient did not have any signs of neovascularization, hence ruling out acquired causes of ectropion uveae. Also, the patient did not have any systemic involvement, thus rendering it as a case of isolated, bilateral congenital ectropion uveae without secondary glaucoma.
|Figure 1: (a and b) High magnified anterior segment slit-lamp photography showing bilateral ectropion uveae with normal iris pattern. (c) Scheimpflug imaging system revealing, ectropion hyperplastic iris tissue in the pupillary border (red arrow). (d and e). Fundus image showing normal disc and retina of OD and OS respectively|
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|Figure 2: (a and b) Slit-lamp photography of gonioscopy revealing open angles with few iris processes of OD and OS respectively|
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Isolated bilateral congenital ectropion uveae is a rare, non-progressive congenital anomaly characterized by the presence of iris pigment hyperplasia on the anterior surface of iris stroma.,, It is induced by primordial endothelium, an embryological remnant that fails to fully regress in the anterior chamber. Keeping in mind that secondary glaucoma, leading to possible blindness precipitates around teenagers in such conditions, a vigilant follow-up was advised, considering the patient was still in his teenage.
Declaration of patient consent
The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.
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Conflicts of interest
There are no conflicts of interest.
| References|| |
Ritch R, Forbes M, Hetherington J Jr, Harrison R, Podos SM. Congenital ectropion uveae with glaucoma. Ophthalmology 1984;91:326-31.
Kolomeyer AM, Kim BJ. Bilateral, presumed congenital ectropion uveae in a patient with pathologic myopia. Am J Ophthalmol Case Rep 2018;11:119-20.
Wilson ME. Congenital iris ectropion and a new classification for anterior segment dysgenesis. J Pediatr Ophthalmol Strabismus 1990;27:48-55.
[Figure 1], [Figure 2]