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OPHTHALMIC IMAGE
Year : 2021  |  Volume : 1  |  Issue : 3  |  Page : 452

Quadrantic lamellar lens opacity - Rule out Stickler!


1 Department of Ophthalmology, Aravind Eye Hospital, Puducherry, India
2 Department of Neuro Ophthalmology and Low Vision Services, Aravind Eye Care, Puducherry, India

Date of Web Publication02-Jul-2021

Correspondence Address:
Dr. Priya Sivakumar
Department of Neuro Ophthalmology and Low Vision Services, Aravind Eye Care, Puducherry - 605 007
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/ijo.IJO_129_21

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How to cite this article:
Rai V, Parab A, Sivakumar P. Quadrantic lamellar lens opacity - Rule out Stickler!. Indian J Ophthalmol Case Rep 2021;1:452

How to cite this URL:
Rai V, Parab A, Sivakumar P. Quadrantic lamellar lens opacity - Rule out Stickler!. Indian J Ophthalmol Case Rep [serial online] 2021 [cited 2021 Jul 26];1:452. Available from: https://www.ijoreports.in/text.asp?2021/1/3/452/319979



A 34-year-old man presented with complaints of defective vision in both eyes with no known systemic illness and no history of trauma. His BCVA in right eye was 6/12 and in left eye was 6/9. Anterior segment examination revealed bilateral temporal lamellar cortical lenticular opacity [Figure 1]a and [Figure 1]b, characteristic sign of Stickler syndrome.[1] Other features of stickler syndrome are multiple pigmented radial lattices on retina,[2] congenital myopia,[1] glaucoma due to angle anomalies,[1] typical facial features consists of mid-facial hypoplasia, depressed nasal bridge, micrognathia and anteverted nares,[3] musculoskeletal features include joint spondyloperipheral dysplasia, hypermotility and early-onset osteoarthritis,[4] hearing loss.[1] Bilateral zonal cataracts are usually idiopathic but are also associated with hereditary disorders and maternal vitamin D deficiency.[5]
Figure 1: (a) Showing quadrantic lamellar cataract in temporal part of lens in right eye. (b) Showing quadrantic lamellar cataract in temporal part of lens in left eye

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Declaration of patient consent

The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.

Financial support and sponsorship

Nil.

Conflicts of interest

There are no conflicts of interest.



 
  References Top

1.
Snead MP, McNinch AM, Poulson AV, Bearcroft P, Silverman B, Gomersall P, et al. Stickler syndrome, ocular-only variants and a key diagnostic role for the ophthalmologist. Eye (Lond) 2011;25:1389-400.  Back to cited text no. 1
    
2.
Vu CD, Brown J, Körkkö J, Ritter R, Edwards AO. Posterior chorioretinal atrophy and vitreous phenotype in a family with stickler syndrome from a mutation in the COL2A1 gene. Ophthalmology 2003;110:70-7.  Back to cited text no. 2
    
3.
Goyal M, Kapoor S, Ikegawa S, Nishimura G. Stickler syndrome type 1 with short stature and atypical ocular manifestations. Case Rep Pediatr 2016;2016:3198597.  Back to cited text no. 3
    
4.
Couchouron T, Masson C. Early-onset progressive osteoarthritis with hereditary progressive ophtalmopathy or Stickler syndrome. Jt Bone Spine 2011;78:45-9.  Back to cited text no. 4
    
5.
Taylor D. The Doyne lecture. Congenital cataract: The history, the nature and the practice. Eye 1998;12:9-36.  Back to cited text no. 5
    


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