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 Table of Contents  
Year : 2021  |  Volume : 1  |  Issue : 1  |  Page : 7

Congenital keratopellis

1 Department of Ophthalmology, Post Graduate Institute of Medical Education and Research, Chandigarh, India
2 Department of Anesthesia, Post Graduate Institute of Medical Education and Research, Chandigarh, India

Date of Web Publication31-Dec-2020

Correspondence Address:
Dr. Jagat Ram
Advanced Eye Center, Post Graduate Institute of Medical Education and Research, Chandigarh - 160 012
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Source of Support: None, Conflict of Interest: None

DOI: 10.4103/ijo.IJO_1822_20

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How to cite this article:
Balamurugan R, Gupta PC, Sethi S, Kaur S, Ram J. Congenital keratopellis. Indian J Ophthalmol Case Rep 2021;1:7

How to cite this URL:
Balamurugan R, Gupta PC, Sethi S, Kaur S, Ram J. Congenital keratopellis. Indian J Ophthalmol Case Rep [serial online] 2021 [cited 2021 Mar 3];1:7. Available from: https://www.ijoreports.in/text.asp?2021/1/1/7/305512

A 4-month-old boy presented to the clinic with bilateral cleft lip and palate. On examination, there was a right lower lid coloboma with the skin on the right side of the upper cheek attached to the right cornea in the form of a band [Figure 1]. Congenital Keratopellis (a novel term coined from Greek: Kerato = cornea; Latin: pellis = skin) is a rare congenital condition wherein the skin is attached to the cornea. Midline facial anomalies such as cleft lip and palate are the second most common congenital anomalies after congenital talipes equinovarus. It may involve other facial structures like eyes, nose, ears, teeth, cheek, brain, etc. They are reported to be associated with the non-syndromic as well as syndromic conditions such as Treacher Collins, Goldenhar, ocular hypertelorism, etc. Embryologically eye is formed from an extension of the neuroectoderm, surrounding mesenchyme and surface ectoderm, and hence any insult occurring in surrounding structures is also invariably associated with ocular malformations. Among the ocular abnormalities (i.e., 8.3%), cleft lip and palate were found to be associated with eyelid coloboma, ectropion, and symblepharon.[1],[2] There are many environmental factors as well as teratogens that are known to affect the normal embryogenesis, which results in the congenital anomalies.[3] In our case, surgical separation of the skin and cornea was done, and subsequently, surgery for cleft lip and cleft palate correction was planned.
Figure 1: Right lower eyelid coloboma with the skin of the cheek attached to the lower half of the cornea

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Declaration of patient consent

The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.

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Conflicts of interest

There are no conflicts of interest.

  References Top

Onwochei BC, Simon JW, Bateman JB, Couture KC, Mir E. Ocular colobomata. Surv Ophthalmol 2000;45:175-94.  Back to cited text no. 1
Anchlia S, Rao KS, Bonanthaya K, Anupama B, Nayak IV. Ophthalmic considerations in cleft lip and palate patients. J Maxillofac Oral Surg 2011;10:14-9.  Back to cited text no. 2
Poswillo D. The aetiology and surgery of cleft palate with micrognathia. Ann R Coll Surg Engl 1968;43:61-88.  Back to cited text no. 3


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