|Year : 2021 | Volume
| Issue : 1 | Page : 14
Posterior lenticonus (lentiglobus) in a 13-year-old child
Parul Jain, Ritu Arora
Guru Nanak Eye Centre, Maulana Azad Medical College, New Delhi, India
|Date of Web Publication||31-Dec-2020|
Dr. Parul Jain
Guru Nanak Eye Centre, Maulana Azad Medical College, New Delhi - 110 002
Source of Support: None, Conflict of Interest: None
|How to cite this article:|
Jain P, Arora R. Posterior lenticonus (lentiglobus) in a 13-year-old child. Indian J Ophthalmol Case Rep 2021;1:14
A 13-year-old male presented to the hospital complaining of bilateral cloudy vision since childhood. Ocular examination revealed best-corrected visual acuity (BCVA) of 20/60 bilaterally. Slit-lamp examination and biomicroscopy of both the eyes were within normal limits except for advanced posterior lenticonus. Oil droplet sign was appreciated on retroillumination [Figure 1]. A provisional diagnosis of Alport syndrome was made and the patient underwent a urine microscopic analysis for hematuria and renal ultrasonography. The child was not found to have any systemic comorbidity. The child was advised to undergo bilateral lens aspiration with intraocular lens (IOL) implantation to manage low vision. The prevalence of posterior lenticonus is estimated at 1–4 in 100,000 children.,
|Figure 1: Posterior lenticonus on retroillumination on slit-lamp examination|
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Posterior lenticonus is characterized by a spherical deformity of the posterior surface of the lens. Clinically, an “oil droplet” red reflex is seen. Posterior lenticonus usually occurs as a sporadic, unilateral anomaly. Other, rare ocular associations include microphthalmos, microcornea, persistent anterior hyaloid vasculature, and uveal colobomas. Posterior lenticonus may also occur as a part of Alport syndrome and the oculocerebrorenal syndrome of Lowe. Any patient presenting with decreased vision and classical lentiglobus (posterior lenticonus) should be suspected to have systemic abnormalities and evaluated accordingly.
Declaration of patient consent
The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.
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Conflicts of interest
There are no conflicts of interest.
| References|| |
Colville DJ, Savige J. Alport syndrome: A review of the ocular manifestations. Ophthalmic Genet 1997;18:161-73.
Vedantham V, Rajagopal J, Ratnagiri PK. Bilateral simultaneous anterior and posterior lenticonus in Alport's syndrome. Indian J Ophthalmol 2005;53:212-3.
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