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OPHTHALMIC IMAGE
Year : 2021  |  Volume : 1  |  Issue : 1  |  Page : 11

Complete Schwalbe's ring in Axenfeld-Rieger anomaly


Department of Ophthalmology, Advanced Eye Centre, Postgraduate Institute of Medical Education and Research, Chandigarh, India

Date of Web Publication31-Dec-2020

Correspondence Address:
Dr. Sushmita Kaushik
Department of Ophthalmology, Advanced Eye Centre, Postgraduate Institute of Medical Education and Research, Chandigarh - 160 012
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/ijo.IJO_2268_20

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How to cite this article:
Snehi S, Gupta G, Dhingra D, Kaushik S. Complete Schwalbe's ring in Axenfeld-Rieger anomaly. Indian J Ophthalmol Case Rep 2021;1:11

How to cite this URL:
Snehi S, Gupta G, Dhingra D, Kaushik S. Complete Schwalbe's ring in Axenfeld-Rieger anomaly. Indian J Ophthalmol Case Rep [serial online] 2021 [cited 2021 Mar 5];1:11. Available from: https://www.ijoreports.in/text.asp?2021/1/1/11/305519



Her parents brought an 18-month-old girl with complaints of a worm-like structure in both eyes. Slit-lamp evaluation revealed a complete Schwalbe's ring (arrow, [Figure 1]), iris hypoplasia, and corectopia. Intraocular-pressure was 14 mm Hg, and optic discs were healthy, in both eyes. Gonioscopy revealed iris processes and iridocorneal adhesions (arrowheads, [Figure 1]) typical of  Axenfeld anomaly More Details.
Figure 1: Slit-lamp and gonioscopy photographs of right and left eye (Right and Left Panel, respectively) showing a complete Schwalbeæs ring (arrows), and iris processes typical of Axenfeld-Rieger anomaly (arrow-heads)

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An anteriorly displaced and prominent Schwalbe's line, also known as “posterior embryotoxon”, may manifest as complete Schwalbe's ring.[1] Typical Axenfeld-Rieger anomaly is defined as the presence of posterior embryotoxon with iris changes like stromal hypoplasia, corectopia, polycoria, or ectropion uvea. Atypical presentations may have overlapping features of other anterior segment dysgenesis, including aniridia, iridocorneal endothelial syndrome, Peters anomaly, and isolated trabeculodysgenesis.[2]  Axenfeld-Rieger syndrome More Details includes systemic abnormalities such as dental, cardiac, craniofacial, and abdominal-wall-defects.[3] No systemic abnormalities were seen in the present case. Informed consent has been obtained from parents of the patient. Ethics approval for this case report has been obtained from Institutional Ethics Committee of 'Post Graduate Institute of Medical Education and Research' (Reference no: NK/6399/Study/745).

Declaration of patient consent

The authors certify that they have obtained all appropriate patient consent forms. In the form the patient(s) has/have given his/her/their consent for his/her/their images and other clinical information to be reported in the journal. The patients understand that their names and initials will not be published and due efforts will be made to conceal their identity, but anonymity cannot be guaranteed.

Financial support and sponsorship

Nil.

Conflicts of interest

There are no conflicts of interest.



 
  References Top

1.
Thurschwell LM, Michelson MA. Axenfeld's anomaly and related disorders. J Am Optom Assoc 1986;57:360-5.  Back to cited text no. 1
    
2.
Rao A, Padhy D, Sarangi S, Das G. Unclassified axenfeld-rieger syndrome: A case series and review of literature. Semin Ophthalmol 2018;33:300-7.  Back to cited text no. 2
    
3.
Seifi M, Walter MA. Axenfeld-Rieger syndrome. Clin Genet 2018;93:1123-30.  Back to cited text no. 3
    


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